Congenital duplication of the anterior segment with central hamartomatous plaque.

A child born of a full-term pregnancy had unilateral splitting of the anterior segment of the right eye associated with choristoma. No other craniofacial abnormalitieswere found. The globe was slightly increased in size but was normal in shape. The 2 corneas were separated by a choristoma. Pathological examination revealed splitting of the anterior segment with 2 corneas, 2 lenses, and 2 irides. Only 1 posterior segment was observed, including a hematic vitreous associated with a dysmorphic retina. As diplophthalmos, this congenital malformation may be induced by primary optic vesicle development disturbance.